Hi, this is Tom and in this episode I'm going to be going through Epstein's Anomily.

And you can find notes at zero to finals.com and in the zero to finals pediatrics book.

And you can find flashcards and questions to train your knowledge at members.0.0 tofinals.com.

And if you stick around to the end of the episode, there'll be questions to test your knowledge

on what you just heard. So let's jump straight in.

Epstein's Anomily is a congenital heart condition where the tricuspid valve is set lower in the right side of the heart

towards the apex of the heart which causes a bigger right atrium and a smaller right ventricle.

The tricuspid valve does not function normally and this results in tricuspid regurgitation,

meaning blood flowing back from the right ventricle to the right atrium.

There is reduced right ventricular function.

Epstein's anomaly is often associated with an atrial septal defect and a right to left shunt.

Blood flow from the right atrium to the left atrium allows blood to bypass the lungs

and this results in cyanosis, which is where deoxygenated blood enters the systemic circulation.

Epstein's Anomily is also often associated with Wolf-Parkinson-White syndrome and superventricular tachycardia.

Let's go through the presentation.

Epstein's Anomily may be asymptomatic until adolescence or adulthood.

It may present with arrhythmias, for example superventricular tachycardia, heart failure,

for example with symptoms of shortness of breath and edema, collapse or cardiac arrest,

and cyanosis when there is an associated atrial septal defect.

Finally, let's talk about management.

An echocardiogram confirms the diagnosis.

Medical management involves treating arrhythmias and heart failure,

...